Thrombotic Microangiopathies » ADAMTS13 and TTP

Abstract Number: PB1882

Acquired Thrombotic Thrombocytopenic Purpura: Key Findings of Patients from Southern Italy

G.L. Tiscia¹, F. Cappucci¹, L. Fischetti¹, C. Battista², A. Ostuni², G. Giordano³, G. Tarantini⁴, T.M. Santeramo⁴, G. Giuffrida⁵, D. Nicolosi⁵, P.R. Scalzulli⁶, N. Cascavilla⁶, L. di Mauro⁷, E. Grandone¹

Abstract Number: OC 07.2

ADAMTS13 Conformation Is Closed in Acquired Thrombotic Thrombocytopenic Purpura in the Absence of Anti-ADAMTS13 Autoantibodies

E. Roose¹, B.S. Joly^2,3, A.-S. Schelpe¹, I. Pareyn¹, A. Vandenbulcke¹, C. Tersteeg¹, S.F. De Meyer¹, P. Coppo⁴, A. Veyradier^2,3, K. Vanhoorelbeke¹

Abstract Number: PB1885

Association of Plasmic Score with Neurological Symptoms in Patients with Thrombotic Thrombocytopenic Purpura (TTP)

J.T.d.S. Castro¹, B.D.M. Mazetto², A.P. Rosa², G. Yamagutti³, M. Colella³, E.V. Paulo³, J.A. Bizachi³, F. Reis¹, F.A. Orsi³

Abstract Number: PB1862

Automated Chemiluminescent ADAMTS13 Activity Immunoassay for Thrombotic Thrombocytopenic Purpura Diagnosis and Follow-up

N. Beranger^1,2, S. Benghezal^1,2, B. Joly^1,2, S. Capdenat^1,2, A. Delton^1,2, A. Stepanian^1,2, P. Coppo³, A. Veyradier^1,2

Abstract Number: PB1863

Caplacizumab in a Case of Acquired Thrombotic Thrombcytopenic Purpura (TTP) Poor Responsive to Plasma Exchange and Immunosuppressive Therapy

A. Molteni, C. Dellanoce, A. Pasini, O. Paoletti, A. Mancini, V. Cancelli, M. Tajana, M. Tala, S. Belletti, R. Morandini, C. Fiamenghi, P. Spedini, S. Testa

Abstract Number: PB1867

Clinical Analysis of 83 Patients with Thrombotic Thrombocytopenic Purpura

W. Xiyan, L. Xiaofan, X. Feng, L. Wei, C. Yunfei, H. Yueting, F. Rongfeng, Z. Lei, Y. Renchi

Abstract Number: PB1889

Clinical and Economic Impacts of a New Rapid ADAMTS-13 Assay for the Diagnosis of Suspected Thrombotic Thrombocytopenic Purpura

C. Novelli¹, B. Montaruli², L. Solfietti³, A. Valpreda⁴, M. Bazzan³, B. Basolo³, I.L.A. Beverina¹, M. Milan⁵, B. Brando¹

Abstract Number: PB1884

Correlation between Phenotype-genotype versus in-silico Prediction of Novel and Known Disease-causing Variants in Upshaw-Schulman Syndrome Patients in a Single Institution of Argentina

J. Paiva¹, A.I. Woods², A. Kinen¹, M.M. Casinelli¹, A. Sanchez-Luceros^1,2

Abstract Number: PB1864

Current Possibilities of ADAMTS 13 Diagnostics – Advantages and Limitations

P. Bradacova¹, L. Slavik², J. Ulehlova², J. Prochazkova², A. Hlusi², K. Chasakova³

Abstract Number: PB1871

Development and Validation of a Prediction Model (AHC) for Early Identification of Refractory Thrombotic Thrombocytopenic Purpura Using Nationally Representative Data

Q.-S. Huang^1,2,3, R.-Y. Gui^1,2,3, Y. Liu⁴, H. Liu⁵, M.-Y. Fang⁶, L.-H. Yang⁷, J.-Y. Zhang⁸, Y.-F. Cheng⁹, M. Jiang¹⁰, M. Mao¹¹, L.-R. Wang¹², Z. Wang¹³, H.-B. Zhou¹⁴, H. Lan¹⁵, Z.-X. Jiang¹⁶, X.-L. Shen¹⁷, L. Zhang¹⁸, S.-J. Fan¹⁹, X.-J. Huang^1,2,3, X.-H. Zhang^1,2,3

Abstract Number: PB1857

Differential Diagnosis of Thrombotic Thrombocytopenic Purpura at Acute Phase by the Ratio of VWF Activity to VWF Antigen Based on Automatic Immunologic Assays

N. Tang

Abstract Number: PB1877

Efficacy of Preemptive Subcutaneous Rituximab in Immune-Mediated Thrombotic Thrombocytopenic Purpura: A Study of 12 Cases

M. Delrue^1,2, M.-T. Baylatry³, A.-C. Joly³, Z. Mmarjanovic³, N. El-Khoury-Hanna⁴, F. Feger⁵, A. Veyradier^1,2, A. Stepanian^1,2, P. Coppo^6,7

Abstract Number: PB1888

Evaluation of a Rapid, Automated Chemiluminescent ADAMTS-13 Activity Assay for the ACL AcuStar

R.E. Fretwell, T. Pitchford, S. Cooper, S. Kitchen

Abstract Number: PB1861

Exploration of Coagulation Disorders, von Willebrand Factor and ADAMTS13 in a Cohort of 45 Patients with Hemophagocytic Lymphohistiocytosis

A. Launois^1,2, S. Valade³, E. Roose⁴, E. Mariotte³, M. Darmon³, L. Galicier⁵, L. Zafrani³, V. Lemiale³, E. Azoulay³, S. Mathis⁶, I. Kalidi⁶, A. Stepanian^1,2, K. Vanhoorelbeke⁴, A. Veyradier^1,2, B. Joly^1,2

Abstract Number: PB1872

Follow-up Evaluation of Patients with Hereditary Thrombotic Thrombocytopenic Purpura (hTTP) from the International Hereditary TTP Registry: Incidence of Acute Disease Episodes with or without Regular Prophylactic Plasma Infusions

E. Tarasco^1,2, L. Bütikofer³, G. Sinkovits⁴, Z. Prohászka⁴, A.S. von Krogh⁵, P.N. Knöbl⁶, K.D. Friedman⁷, J.N. George⁸, I. Aebi-Huber^1,2, K.A. Jalowiec¹, Z. Cermakova⁹, M. Górska-Kosicka¹⁰, J. Windyga¹⁰, I. Hrachovinova¹¹, C.R. Largiadèr¹², M. Matsumoto¹³, B. Lämmle^1,14, J.A. Kremer Hovinga^1,2

Abstract Number: PB1874

Genetic Study of von Willebrand Factor Variants in Congenital Thrombotic Thrombocytopenic Purpura Patients

C. Lupo¹, C. Vendramin¹, F. Alwan², M. Scully^1,2

Abstract Number: PB1890

Genetic Variants in ADAMTS13 in Patients with Acquired TTP (aTTP)

J. Paiva¹, A.I. Woods², A. Kinen¹, M.M. Casinelli¹, A. Sanchez-Luceros^1,2

Abstract Number: OC 07.1

How to Open ADAMTS13: An Integrative Approach to Build ADAMTS13 in Closed Conformation

B. Ercig^1,2, N.A.G. Graca^1,3, K. Wichapong², E. Roose⁴, P. Kaijen¹, T. Arfman¹, C. Reutelingsperger², K. Vanhoorelbeke⁴, G.A.F. Nicolaes², J. Voorberg¹

Abstract Number: PB1891

Impact of Ultralarge von Willebrand Factor (VWF) Multimers and Platelets in Cultured Endothelial Cells in Acute Immune-mediated Thrombotic Thrombocytopenic Purpura

C. Vendramin¹, F. Patella², C. Lupo¹, D. Cutler², M. Scully^1,3

Abstract Number: PB1879

Influence of Personality and Life Conditions on Depression, Anxiety and Cognitive Performance in 104 Patients Having Survived Acute Autoimmune Thrombotic Thrombocytopenic Purpura (iTTP)

T. Falter¹, S. Boeschen¹, M. Beutel², K. Lackner¹, B. Lämmle^3,4,5, I. Scharrer³